Monomelic Ulnar Dimelia Associated with Ipsilateral Polydactyly: An Extraordinary Anomaly

Ulnar dimelia (mirror deformity) is a rare dysontogenetic deformity of the upper limb caused by an embryonic disturbance of the developing limb bud. It is characterized by two ulnae, the duplication of the ulnar halves of the carpus, metacarpals and phalanges, with the absence of the radius and thumb. It is commonly unilateral. This anomaly may be associated with shoulder dislocation, fibular dimelia, idiopathic scoliosis, cirrhosis, pyloric hypertrophy or a polycystic kidney. Approximately 72 cases have been reported since it was first described in 1587 . We herein describe a rare case of ulnar dimelia associated with ipsilateral polydactyly.